About PH
In this section, you will find videos and resources that cover the basics of PH, including the different types, diagnosis and information on research. Select a topic from the list below to begin learning about PH.
Fundamentals of Genetic Testing
Watch the webinar recording to review an overview of genetics and genetic testing in pulmonary hypertension. Learn about types of genetic tests, interpreting test results and the risks and benefits of genetic testing. In this recording, speakers also review who is considered eligible for genetic testing in heritable pulmonary arterial hypertension.
10 Facts You Should Know About CTEPH
William R. Auger shares 10 important facts pulmonary hypertension patients should know about CTEPH. Dr. Auger highlights how chronic thromboembolic pulmonary hypertension is diagnosed, the signs to look for and the latest treatment available.
Understanding the Connection between Idiopathic Pulmonary Fibrosis and PH
Navneet Singh, MD, MBA, and Christopher King, MD, discuss the tests needed for an accurate IPF and PH diagnosis and the latest treatment options available for each disease.
Respiratory Infections and Pulmonary Hypertension
Ivan Robbins, M.D., and Nidhy Varghese, M.D., discuss the impact viral respiratory infections have on adults and children with PH. They share information on the symptoms of viral infections, the impact of RSV on children and older adults with PH and give an overview of how to treat these conditions safely while on PH medication.
What’s the Relationship Between Scleroderma and PH?
Stephen Mathai, M.D., M.H.S, discusses scleroderma and how it’s characterized in the body. Dr. Mathai also talks about the risk of developing pulmonary arterial hypertension or interstitial lung disease related to scleroderma.
What Treatments are Prescribed to Manage PH and Connective Tissue Disease?
Stephen Mathai, M.D., M.H.S, discusses the importance of working with your health care team when treating pulmonary hypertension (PH) and connective tissue disease. Dr. Mathai gives an overview of considerations that should be evaluated when making treatment decisions for patients with connective tissue diseases and pulmonary hypertension.
What is the Relationship Between PH and Connective Tissue Disease?
Stephen Mathai, MD, MHS explains the relationship that exists between pulmonary hypertension and connective tissue disease.
What is the Risk of Developing PH if You Have Connective Tissue Disease?
Stephen Mathai, MD, MHS discusses the various risks related to developing pulmonary hypertension if you have connective tissue disease.
PH101: Part 1- Understanding Diagnosis
Jean M. Elwing, MD presents information on the basics of PH, how PH is defined and the types and classifications of PH.
Group 3 Pulmonary Hypertension
Shilpa Johri, MD
Group 2 Pulmonary Hypertension
Gautam V. Ramani, MD
What is PH?
Javier Jimenez, MD
What happens when you have PH?
Javier Jimenez, MD
What are the symptoms of PH?
Javier Jimenez, MD
CTEPH Overview
Gustavo Heresi, MD
What are the different WHO Groups of pulmonary hypertension?
Amresh Raina, MD, FACC
What are the functional classifications of PH?
Amresh Raina, MD, FACC
Are there specific lung diseases that cause PH?
Rana Awdish, MD
What is PH due to chronic lung disease?
Rana Awdish, MD
How does lung disease cause pulmonary hypertension?
Rana Awdish, MD
How does liver disease cause PH?
Hilary M. DuBrock, MD
How is the liver connected to the heart and lungs?
Hilary M. DuBrock, MD
Understanding Genetic Risks in Pulmonary Arterial Hypertension
Carrie Welch, assistant professor of pediatrics, explains how gene mutations in heritable pulmonary arterial hypertension can cause PAH to develop in families. Watch the video to learn the role of genetic testing in identifying gene variants in adult and childhood onset heritable PAH. In addition, Welch explains the types of PAH gene testing, the role of genetic counselors, questions you should ask regarding PAH genetic test results and steps to take after PAH genetic testing.
Journey through Pulmonary Hypertension Diagnosis and Treatment
Christina Benninger, M.S.N., APRN, FNP-BC, AGACNP-BC explains the pulmonary hypertension (PH) diagnostic process and what the test results can provide to clinicians. Find out why understanding the results of echocardiograms, right heart catheterizations and other imaging techniques and lab tests is essential to determining effective PH treatment.
What are the different types of connective tissue disease and the associated risk of PH?
Stephen Mathai, MD, MHS discusses different types of connective tissue disease including lupus, Sjogren’s syndrome, polymyositis, and rheumatoid arthritis and the associated risk of having pulmonary hypertension.
What diagnostic tests are recommended for patients with connective tissue disease?
Stephen Mathai, MD, MHS discusses connective tissue disease and the various diagnostic tests used to assess patients with connective tissue disease for pulmonary hypertension.
Visiting a Genetic Counselor
Emily Griffin, M.S., C.G.C, a genetic counselor from Columbia University Irving Medical Center explains the basics of a genetic counseling session including what to expect and how to prepare for an appointment.
Can a chest x-ray diagnose PH?
Amresh Raina, MD, FACC
Why do I need a right heart catheterization if my doctor gets numbers from the echocardiogram?
Amresh Raina, MD, FACC
How is PH diagnosed?
Amresh Raina, MD, FACC
Why do I have to do the 6-minute walk test? What does it tell my doctor?
Amresh Raina, MD, FACC
Why is it important to know which WHO Group your diagnosis is in?
Amresh Raina, MD, FACC
What is a V/Q scan? Should all PH patients have one?
Amresh Raina, MD, FACC
What do blood tests tell my doctor about my PH?
Amresh Raina, MD, FACC
What value does a cardiac MRI bring to diagnosis and treatment?
Amresh Raina, MD, FACC
Is there a standard for how often I should have certain diagnostic testing? How does this vary, or does it depend on the doctor?
Amresh Raina, MD, FACC
After my first right heart cath, how often do I need to have another one, and why?
Amresh Raina, MD, FACC
How often do I have to have an echocardiogram?
Amresh Raina, MD, FACC
Newly Diagnosed: Tests, Tests and More Tests: What Is PH Diagnostic Testing Telling My Doctors?
Deedre’ Boekweg, RN, MSN, CCRP
All the testing that goes into a correct PH diagnosis can be overwhelming! This webinar reviewed and dissected many of the clinical tests that are used in the diagnosis of pulmonary hypertension, including: echocardiogram, right heart cardiac catheterization, pulmonary function testing, sleep studies and other laboratory tests. The session also discussed the risks and benefits of the testing, as well as how all the information is used to unravel different diagnoses of pulmonary hypertension.
Assessing Risk in Pulmonary Arterial Hypertension: Is Your Treatment Plan Working?
Risk assessment for pulmonary arterial hypertension plays an important role in your overall care plan. View this video series to understand PAH risk assessment as a tool in your treatment plan; what to expect during an assessment; and the importance of managing your PAH with your health care team.
Treating and Managing PH: What You Need to Know
J. Wesley McConnell, M.D. encourages patients to speak up and ask questions during medical appointments, to maintain an open and collaborative partnership with their healthcare team to achieve successful outcomes together.
Understanding the Side Effects of Pulmonary Hypertension Medication
Gillian Leung, PharmD, BCCP; Yash Kothari, M.D. cover common side effects of pulmonary hypertension (PH) medications. Drs. Leung and Kothari share tips for managing undesirable effects to get the most out of PH therapy.
PH101: Part 2 – Diagnostics and Treatment Options
Jean M. Elwing, MD discusses the different types of PH and the reasons behind the extensive testing that is required for an accurate PH diagnosis. An explanation of the available treatments for each type of PH and considerations that your PH care team makes when choosing the best treatment plan for you is presented.
What contributes to the success of treatment for PH?
Javier Jimenez, MD
How is PH treated?
Javier Jimenez, MD
CTEPH Treatment
Gustavo Heresi, MD
Tell me more about lung transplantation: What is it all about, and what is involved?
Fernando Torres, MD
How is portopulmonary hypertension treated?
Hilary M. DuBrock, MD
Hope Through Research in Pulmonary Hypertension: Clinical Trials
Health care professionals, Alejandro Cruz Eric Austin, Maria Jesus del Cerro Marin alongside Matt Granato, President & CEO, PHA and Enrique Carazo MÃnguez, President, FCHP provides an overview of the clinical trial process, how adult and pediatric trials differ and the importance of PH patients volunteering to participle in clinical studies. Principal investigators conducting some of the exciting clinical trials in the PH pipeline shared details about the new pathways and approaches to treating PH as well as how to volunteer for these and other clinical studies.
Hope Through Research in Pulmonary Hypertension: Emerging Developments
Health care professionals, Anna R. Hemnes, Matthew Lammi, Catherine Simpson, and PH patient, Julia Feitner share the latest pulmonary hypertension research and clinical studies. Learn about keyresearch developments and how they may impact PH patients in the future. PH patient, Julia Feitner shares her experience of participation in a clinical trial and why she volunteered to advance PH research.
Spotlight on Pulmonary Hypertension Clinical Studies and Research
J. Wes McConnell, M.D., explains how research process and can lead to promising clinical trials for new therapies and how patient registries can advance pulmonary hypertension. Dr. McConnell also shares news about how to participate in regional clinical trials.
2022 Focus on Pulmonary Hypertension Research
Pulmonary hypertension experts Anna Hemnes, M.D., and Evan Brittain, M.D., M.Sc., moderate a panel discussion on the latest advances in pulmonary hypertension (PH) research.
Part 1: Understanding the PH Drug Pipeline
Part 1 of Understanding the PH Drug Pipeline presented by Pulmonologist Anna R. Hemnes, M.D, provides insight on available PAH therapies, the biological pathways through which drugs are targeted and new treatments in the drug development pipeline.
Part 2: Understanding the PH Drug Pipeline Q&A
Part 2 of Understanding the PH Drug Pipeline presented by Pulmonologist Anna Hemnes, MD answers questions and provides insight on the available PAH therapies, the biological pathways targeted and new treatments in the drug development pipeline during this Q&A portion.
An Overview of the Drug Development Process
Daniel C. Grinnan, MD, provides an overview of how new medications are developed.
Debunking Myths and Misconceptions About Clinical Trial Participation
Rachel Damico, MD, PhD, addresses common concerns about clinical trial participation and the risks and benefits of participating in clinical research.
Clinical Research in Pediatrics and Informed Consent for Parents
Melanie K. Nies, MD, talks about why pediatric research is important, how it is different than research in adults and things to know when considering participation in pediatric research for your child.
What Is FDA Approval?
Daniel C. Grinnan, MD, explains the U.S. Food and Drug Administration (FDA) and its role in drug approval.
What Is Clinical Research?
Andrea Mytinger, DO, talks about the different types of clinical research, the steps needed to complete a clinical trial and the importance of clinical research.
Getting Involved in Clinical Research
Christopher S. King, MD, discusses how to talk to your doctor about getting involved in clinical research and explains the informed consent process.
