Idiopathic pulmonary fibrosis (IPF) is the most common type of interstitial lung disease (ILD). ILDs are characterized by scarring and/or inflammation in the interstitium, the support tissue in the lungs that sits between the blood vessels and the air sacs.
Patients with IPF can develop pulmonary hypertension (PH) for many reasons, including a stiff left side of the heart or sleep apnea. IPF patients who develop PH tend to report worse breathing problems, lower extremity swelling or dizziness with activity. It is important to rule out sleep apnea and chronic blood clots in the lungs caused by CTEPH and to identify whether left heart issues are involved. This is accomplished through a variety of diagnostic tests.
Download the Pulmonary Hypertension Association (PHA)’s free patient brochure to learn more about PH risks and treatment options.